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投稿を見ていただきありがとうございます! 今回は 【点頭てんかん(ウエスト症候群)】 についててんかん専門医がお答えします! ↓↓↓ ——————————— 点頭てんかん(ウエスト症候群)とは ——————————— <特徴> ⚫︎しばしば精神運動発達の退行(もともとできていたことができなくなる、元気がなくなり笑顔が消える、など)をきたすてんかん ⚫︎速やかな治療が必要で、抗てんかん発作薬(その組み合わせ)、ACTH治療、ケトン食治療、てんかん外科(手術)など、種々のてんかん治療を要することが少なくない <発症時期> 主に乳児期から幼児期早期に発症 <発症率> 10000万出生のうち数人程度が発症 <生じやすいタイミング> 眠たい状態の時に生じやすい <動きの特徴> ⚫︎間隔は10秒前後、初めは長く次第に短く ⚫︎「しゃっくり」のようにある程度規則的な間隔で生じる ⚫︎ピクっとする動作の際に頭や体が前傾する ⚫︎動作前におとなしくなり、動作後に大きく泣いたりする <どのように診断されるのか> ウエスト症候群(点頭てんかん)は、繰り返し生じる“てんかん性スパズム(点頭発作)”との特徴的な
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投稿を見ていただきありがとうございます! 今回は 【点頭てんかん(ウ …
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